TY - JOUR
T1 - Direct Measurement of Porto-systemic Gradient in a Failing Fontan Circulation
AU - Velpula, Madhavi
AU - Sheron, Nick
AU - Guha, Neill
AU - Salmon, Tony
AU - Hacking, Nigel
AU - Veldtman, Gruschen R.
PY - 2011/3
Y1 - 2011/3
N2 - We describe the case history of a 42-year-old man with cardiac cirrhosis, portal hypertension, and life-threatening variceal bleeding after Fontan revision surgery. Direct pressure measurements in the portal vein, though high, demonstrated only a modest portosystemic gradient (PSG), 9mmHg. A transjugular intrahepatic portosystemic shunt procedure was performed. This reduced the PSG (3mmHg). His bleeding was controlled. The patient's histopathological findings were identical to that previously documented in Fontan patients, raising the question of whether these subdiaphragmatic hemodynamics are representative of the broader failing Fontan population.
AB - We describe the case history of a 42-year-old man with cardiac cirrhosis, portal hypertension, and life-threatening variceal bleeding after Fontan revision surgery. Direct pressure measurements in the portal vein, though high, demonstrated only a modest portosystemic gradient (PSG), 9mmHg. A transjugular intrahepatic portosystemic shunt procedure was performed. This reduced the PSG (3mmHg). His bleeding was controlled. The patient's histopathological findings were identical to that previously documented in Fontan patients, raising the question of whether these subdiaphragmatic hemodynamics are representative of the broader failing Fontan population.
KW - Cardiac Cirrhosis
KW - Fontan Circulation
KW - Portal Hypertension
KW - Transjugular Intrahepatic Portosystemic Shunt
UR - http://www.scopus.com/inward/record.url?scp=79953013838&partnerID=8YFLogxK
U2 - 10.1111/j.1747-0803.2010.00451.x
DO - 10.1111/j.1747-0803.2010.00451.x
M3 - Article
C2 - 21356034
AN - SCOPUS:79953013838
SN - 1747-079X
VL - 6
SP - 175
EP - 178
JO - Congenital Heart Disease
JF - Congenital Heart Disease
IS - 2
ER -